Preview of New ICD-11 Codes Revealed

Original story posted on: August 6, 2018

New codes to be presented at the September Coordination and Maintenance Committee meeting

There is a lot of buzz in the industry about the possibility of ICD-11. We are so many years from that becoming a possibility, though, with our clinical modifications and political culture. And we still have a lot of work to make ICD-10-CM all that we need it to be. It would be disappointing to move to a new code set without making sure all of our coding options have been thought through appropriately. We continue to refine and work on improving ICD-10-CM, and that will only make our efforts for ICD-11 more productive.

Recently I had the pleasure of helping the American Partnership for Eosinophilic Disorders (APFED) work on requesting some new codes, along with some revisions that will be presented at the September Coordination and Maintenance Committee Meeting.

Medicine is constantly evolving, and it’s still important to keep our coding up to date. For this project, it was recognized that some codes in ICD-9-CM were not captured in ICD-10-CM, nor were some terminology changes. What was really interesting is that while some of the codes were missed in ICD-10-CM, they were captured or added in ICD-11. Of the 12 new and 13 revised codes, five of the codes requested are captured in ICD-11. They have also gained the support of several other organizations.

Eosinophils are a type of white blood cell, and they play an important role in our immune system. Eosinophils help us fight off certain types of infections, such as parasites. Eosinophil-associated diseases are chronic and require long-term management. The symptoms may be debilitating and often lead to missed time at school and work, and may greatly impact a patient’s quality of life, according to APFED.

In the organization’s proposal, it cites the need for better research, quoting a recent National Institutes of Health (NIH) article in support:

“A recently published article, Revisiting the NIH Taskforce on the Research needs of Eosinophil-Associated Diseases (RE-TREAD), authored by 27 researchers and clinicians, documented (that) ‘eosinophil-associated diseases are rare, heterogeneous disorders characterized by the presence of eosinophils in tissues and/or peripheral blood resulting in immunopathology...histopathologic scoring, patient- and clinician-reported outcomes, and appropriate coding were deemed of paramount importance for research advancements, drug-development and their approval by regulatory agencies...Unique ICD-10 codes can improve disease management and treatment choices, and may result in improved resource allocation and understanding of unmet needs in rare eosinophilic diseases. From a research perspective, utilization of more specific codes is important for better understanding of prevalence, incidence, treatment, and healthcare utilization associated with these diseases, as well as the identification of subjects for potential recruitment into clinical trials.”Khoury PAkuthota PAckerman SJ


The request includes:


Hypereosinophilic Syndromes


Myeloid Hypereosinophilic Syndrome Without a Known Molecular Abnormality


Myeloid Hypereosinophilic Syndrome with Mutations in PDGFRA, PDGFRB, FGFR1, or JAK2


Lymphoid Variant Hypereosinophilic Syndrome


Idiopathic Hypereosinophilic Syndrome


Hypereosinophilic Syndrome, NOS


Eosinophilic Pneumonia


Acute Eosinophilic Pneumonia


Chronic Eosinophilic Pneumonia


Eosinophilic Asthma


Eosinophilic Hepatitis


Drug Rash with Eosinophilia and Systemic Symptoms (DRESS)


Episodic Angioedema with Eosinophilia (EAE), also Known as Gleich’s Syndrome


Eosinophilic Myositis


Request for Amendments


Eosinophilic Granulomatosis with Polyangiitis


Eosinophilic Gastroenteritis


Eosinophilic Gastritis

Hopefully, the September meeting will generate support for these new codes and revisions so that better data can be tracked, and progress continued. I will be following this proposal in September and then start helping educate our practices on how to use the new codes, along with documentation best practices.


Program Note:


Listen to Rhonda Buckholtz report on topic today on Talk Ten Tuesday, 10 a.m. EDT.

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Disclaimer: Every reasonable effort was made to ensure the accuracy of this information at the time it was published. However, due to the nature of industry changes over time we cannot guarantee its validity after the year it was published.

Rhonda Buckholtz is the vice president of practice optimization for Eye Care Leaders. She has more than 25 years of experience in healthcare, working in the management, reimbursement, billing, and coding sectors, in addition to being an instructor. She is a past co-chair for the WEDI ICD-10 Implementation Workgroup, Advanced Payment Models Workgroup and has provided testimony ongoing for ICD-10 and standardization of data for NCVHS. Rhonda spends her time on practice optimization for Eye Care Leaders by providing transformational services and revenue integrity for Ophthalmology practices. She was instrumental in developing the Certified Ophthalmology Professional Coder (COPC) exam and curriculum for the AAPC. Rhonda is a member of the ICD10monitor editorial board and makes frequent appearances on Talk Ten Tuesdays.

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